Cardiopulmonary involvement in juvenile systemic sclerosis: development of recommendations for screening and investigation

نویسندگان

  • Clare Pain
  • Tamas Constantin
  • Eileen Baildam
  • Christian Beyer
  • Henning Lenhartz
  • Michael Blakley
  • Dana Nemcova
  • Clarissa Pilkington
  • Ivan Foeldvari
چکیده

Introduction There are currently no agreed recommendations on how to investigate children for cardiopulmonary involvement in Juvenile Systemic Sclerosis (JSSc). The aim of screening is to detect disease early to facilitate early aggressive therapy and improve outcomes. Cardiopulmonary involvement is the leading cause of death in JSSc and cardiopulmonary at diagnosis incurs a worse outcome [1]. Most deaths occur early in the disease course [1, 2].

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عنوان ژورنال:

دوره 12  شماره 

صفحات  -

تاریخ انتشار 2014